Retroperitoneal NonFunctioning Paraganglioma with Solitary Sternal Metastasis – A Rare Presentation

Abstract

Paragangliomas are rare and arise from neural crest cells. They are often difficult to diagnose because of varied clinical presentation.

Reporting a case of 47 year male presenting with lower abdominal pain, diagnosed to have a retroperitoneal tumour situated at the aortic bifurcation. Serum catecholamine levels were within normal limits. Complete resection of the tumour was done in June 23. The HPE and IHC analysis was suggestive of intermediate risk paraganglioma. Patient was on regular follow up.

In December 23, he presented with complaints of pain over the sternum . On evaluation , he was found to have a solitary lesion in the sternum , which was DOTA avid. 2 cycles of Lu therapy was tried, but in view of progressive nature of the disease and considering the fact that it was the solitary site of metastasis, he was taken up for sternal resection with reconstruction in Jan 23. Postop HPE was suggestive of a paraganglioma.